Severe congenital factor XIII deficiency caused by novel W187X and G273V mutations in the F13A gene: diagnosis and classification according to the ISTH/SSC guidelines., Haemophilia, 20(2) 255-262, 2014.03

Souri M, Biswas A, Misawa M, Omura H, Ichinose A

Multiple Authorship (Including Foreigners)

Alloantibodies against the B subunit of plasma factor XIII developed in its congenital deficiency., Thrombosis and Haemostasis, 109(4) 661-668, 2013.04

Wada H, Souri M, Matsumoto R, Sugihara T, Ichinose A

Multiple Authorship (Including Foreigners)

Molecular modeling predicts structural changes in the A subunit of factor XIII caused by two novel mutations identified in a neonate with severe congenital factor XIII deficiency., Thrombosis Research, 130(3) 506-510, 2012.09

Souri M, Yee VC, Fujii N, Ichinose A

Multiple Authorship (Including Foreigners)

Increase in the plasma levels of protein Z-dependent protease inhibitor in normal pregnancies but not in non-pregnant patients with unexplained recurrent miscarriage., Thrombosis and Haemostasis, 107(3) 507-512, 2012.05

Souri M, Sugiura-Ogasawara M, Saito S, Kemkes-Matthes B, Meijers JC, Ichinose A

Multiple Authorship (Including Foreigners)

Reduced difference of alpha2-plasmin inhibitor levels between plasma and serum in patients with severe factor XIII deficiency, including autoimmune hemorrhaphilia due to anti-factor XIII antibodies., International Journal of Hematology, 95(1) 47-50, 2012.01

Ichinose A, Souri M

Multiple Authorship (Including Foreigners)

As many as 12 cases with haemorrhagic acquired factor XIII deficiency due to its inhibitors were recently found in Japan., Thrombosis and Haemostasis, 105(5) 925-927, 2011.05

Ichinose A, Souri M; Japanese collaborative research group on "Acquired haemorrha-phillia due to factor XIII deficiency"

Multiple Authorship (Including Foreigners)

Impaired clot retraction in factor XIII A subunit-deficient mice., Blood, 115(6) 1277-1279, 2010.02

Kasahara K, Souri M, Kaneda M, Miki T, Yamamoto N, Ichinose A

Multiple Authorship (Including Foreigners)

Unique secretion mode of human protein Z: its Gla domain is responsible for inefficient, vitamin K-dependent and warfarin-sensitive secretion., Blood, 113(16) 3857-3864, 2009.04

Souri M, Iwata H, Zhang WG, Ichinose A

Multiple Authorship (Including Foreigners)

Sushi domains in the B subunit of factor XIII responsible for oligomer assembly., Biochemistry, 47(33) 8656-8664, 2008.08

Souri M, Kaetsu H, Ichinose A

Multiple Authorship (Including Foreigners)

Male-specific cardiac pathologies in mice lacking either the A or B subunit of factor XIII., Thrombosis and Haemostasis, 99(2) 401-408, 2008.02

Souri M, Koseki-Kuno S, Takeda N, Yamakawa M, Takeishi Y, Degen JL, Ichinose A

Multiple Authorship (Including Foreigners)

Administration of factor XIII B subunit increased plasma factor XIII A subunit levels in factor XIII B subunit knock-out mice., International Journal of Hematology, 87(1) 60-68, 2008.01

Souri M, Koseki-Kuno S, Takeda N, Degen JL, Ichinose A

Multiple Authorship (Including Foreigners)

Regulation of human protein Z gene expression by liver-enriched transcription factor HNF-4alpha and ubiquitous factor Sp1., Journal of Thrombosis and Haemostasis, 5(11) 2250-2258, 2007.11

Sugawara H, Iwata H, Souri M, Ichinose A

Multiple Authorship (Including Foreigners)

An additional Glu30Lys substitution in the Gla domain of the protein Z gene is not a common polymorphism but a rare mutation, which would cause its deficiency., Journal of Thrombosis and Haemostasis, 3(10) 2360-2361, 2005.10

Iwata H, Souri M, Kemkes-Matthes B, Ichinose A

Multiple Authorship (Including Foreigners)

A naturally occurring E30Q mutation in the Gla domain of protein Z causes its impaired secretion and subsequent deficiency., Blood, 105(8) 3149-3154, 2005.04

Souri M, Koseki-Kuno S, Iwata H, Kemkes-Matthes B, Ichinose A

Multiple Authorship (Including Foreigners)

R255h amino acid substitution of protein Z identified in patients with factor V Leiden mutation., British Journal of Haematology, 128(2) 248-252, 2005.01

Kemkes-Matthes B, Matthes KJ, Souri M, Koseki-Kuno S, Ichinose A

Multiple Authorship (Including Foreigners)

Impaired protein folding, dimer formation, and heterotetramer assembly cause intra- and extracellular instability of a Y283C mutant of the A subunit for coagulation factor XIII., Biochemistry, 40(45) 13413-13420, 2001.11

Souri M, Ichinose A

Multiple Authorship (Including Foreigners)

Truncated Mutant B Subunit for Factor XIII Causes its Deficiency due to Impaired Intracellular Transportation., Blood, 97(9) 2667-2672, 2001.05

Koseki S, Souri M, Koga S, Yamakawa M, Shichishima T, Maruyama Y, Yanai F, Ichinose A

Multiple Authorship (Including Foreigners)

Transcriptional regulation of cell type-specific expression of the TATA-less A subunit gene for human coagulation factor XIII., Journal of Biological Chemistry, 274(10) 6138-6147, 1999.05

Kida M, Souri M, Yamamoto M, Saito H, Ichinose A

Multiple Authorship (Including Foreigners)

Relationship between structure and substrate-chain-length specificity of mitochondrial very-long-chain acyl-coenzyme A dehydrogenase., European Journal of Biochemistry, 257(3) 592-598, 1998.11

Masayoshi Souri, Toshifumi Aoyama, Seiji Yamaguchi, and Takashi Hashimoto

Multiple Authorship (Including Foreigners)

A founder effect is proposed for factor XIII B subunit deficiency caused by the insertion of triplet AAC in exon III encoding the second sushi domain., Thrombosis and Haemostasis, 80(2) 211-213, 1998.08

Masayoshi Souri, Tomonori Izumi, Yoichiro Higashi, Antonio Girolami, and Akitada Ichinose

Multiple Authorship (Including Foreigners)

Very-long-chain acyl-CoA dehydrogenase subunit assembles to the dimer form on mitochondrial inner membrane, FEBS Letters, 426（2）: 187-190, FEBS Letters, 426(2) 187-190, 1998.04

Masayoshi Souri, Toshifumi Aoyama, George Hoganson, and Takashi Hashimoto

Multiple Authorship (Including Foreigners)

Catalytic and FAD-binding residues of mitochondrial very long chain acyl-coenzyme A dehydrogenase., Journal of Biological Chemistry, 273(7) 4227-4231, 1998.02

Masayoshi Souri, Toshifumi Aoyama, Gerald F. Cox, and Takashi Hashimoto

Multiple Authorship (Including Foreigners)

Mutation analysis of very-long-chain acyl-coenzyme A dehydrogenase（VLCAD）deficiency：identification and characterization of mutant VLCAD cDNAs from four patients., American Journal of Human Genetics, 58(1) 97-106, 1996.01

Masayoshi Souri, Toshifumi Aoyama, Kohji Orii, Seiji Yamaguchi, and Takashi Hashimoto

Multiple Authorship (Including Foreigners)

Purification of human very-long-chain acyl-coenzyme A dehydrogenase and characterization of its deficiency in seven patients., Journal of Clinical Investigation, 95(6) 2465-2473, 1995.01

Toshifumi Aoyama, Masayoshi Souri, Seiichi Ushikubo, Takehiko Kamijo, Seiji Yamaguchi, Richard I. Kelley, William J. Rhead, Kimiaki Uetake, Kay Tanaka, and Takashi Hashimoto Toshifumi Aoyama, Masayosh...

Multiple Authorship (Including Foreigners)

A sensitive assay of acyl-coenzyme A oxidase by coupling with β-oxidation multienzyme complex., Analytical Biochemistry, 221(2) 362-367, 1994.09

Masayoshi Souri, Toshifumi Aoyama and Takashi Hashimoto

Multiple Authorship (Including Foreigners)